Article: A functional null mutation of SCN1B in a patient with Dravet syndrome.
Full Text (publisher's website) ; Article Metadata ; Article Data (extracted) Patino GA; Claes LR; Lopez-Santiago LF; Slat EA; Dondeti RS; Chen C; O'Malley HA; Gray CB; Miyazaki H; Nukina N; Oyama F; De Jonghe P; Isom LL J. Neurosci., 2009
Scn1b+/+ | Scn1b−/− | |
---|---|---|
CA1 | ||
Resting potential (mV) | −71.99 ± 1.21 | −71.78 ± 0.76 |
Input resistance (MΩ) | 142.60 ± 27.68 | 141.36 ± 11.23 |
Threshold (mV) | −33.81 ± 2.00 | −33.00 ± 1.50 |
Rise time (ms) | 0.76 ± 0.03 | 0.67 ± 0.03 |
Peak voltage (mV) | 35.48 ± 1.91 | 33.73 ± 2.16 |
Amplitude (mV) | 69.29 ± 2.90 | 66.74 ± 2.36 |
n | 22 | 19 |
CA3 | ||
Resting potential (mV) | −72.96 ± 0.54 | −71.74 ± 0.59 |
Input resistance (MΩ) | 156.99 ± 5.97 | 161.75 ± 11.06 |
Threshold (mV) | −33.82 ± 0.75 | −35.73 ± 0.78 |
Rise time (ms) | 0.61 ± 0.02 | 0.52 ± 0.01 |
Peak voltage (mV) | 38.77 ± 1.49 | 46.36 ± 1.21* |
Amplitude (mV) | 72.59 ± 1.60 | 82.10 ± 1.29† |
n | 34 | 21 |