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Article: Neonatal neuronal circuitry shows hyperexcitable disturbance in a mouse model of the adult-onset neurodegenerative disease amyotrophic lateral sclerosis.

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van Zundert B; Peuscher MH; Hynynen M; Chen A; Neve RL; Brown RH; Constantine-Paton M; Bellingham MC
J. Neurosci., 2008


Table 2.

Superior colliculus interneuron properties

mSOD1WT hSOD1G93A
Cell properties
    Resting membrane potential (mV) −61 ± 3 −63 ± 2
    Input resistance (MΩ ) 1061 ± 171 863 ± 145
Action potential properties
    Threshold (mV above resting MP) 26 ± 3 25 ± 3
    Amplitude (mV above threshold MP) 61 ± 8 84 ± 6*
    Maximum rate of AP rise (mV/ms) 109 ± 24 171 ± 26
    Duration (ms) 4.2 ± 0.5 3.1 ± 0.2
    Half-width duration (ms) 1.8 ± 0.2 1.5 ± 0.1
    Afterhyperpolarization amplitude (mV below threshold MP) −21 ± 2 −21 ± 2
    Number of cells 8 7
  • Averaged cell properties and AP properties (analyzed from single AP) are shown for mSOD1WT and hSOD1G93A SCs (P10–P12). AP threshold is relative to resting membrane for each SC recorded; AP and afterhyperpolarization amplitude are relative to AP threshold potential for each SC recorded. Note that only the AP amplitude is significantly increased in hSOD1G93A SCs. Statistical significance (Student's unpaired t test) is indicated. Data are mean ± SEM.


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Inferred neuron-electrophysiology data values

Neuron Type Neuron Description Ephys Prop Extracted Value Standardized Value Content Source
Superior colliculus superficial layer neuron stratum griseum superficiale of superior colliculus interneuron resting membrane potential (mV) -61.0 ± 3.0 (8) -61.0 (mV) Data Table
Superior colliculus superficial layer neuron stratum griseum superficiale of superior colliculus interneuron input resistance (MΩ ) 1061.0 ± 171.0 (8) 1061.0 (MΩ) Data Table
Superior colliculus superficial layer neuron stratum griseum superficiale of superior colliculus interneuron spike threshold 26.0 ± 3.0 (8) -26.0 (mV) Data Table
Superior colliculus superficial layer neuron stratum griseum superficiale of superior colliculus interneuron spike amplitude 61.0 ± 8.0 (8) 61.0 (mV) Data Table
Superior colliculus superficial layer neuron stratum griseum superficiale of superior colliculus interneuron spike max rise slope (mV/ms) 109.0 ± 24.0 (8) 109.0 (mV/ms) Data Table
Superior colliculus superficial layer neuron stratum griseum superficiale of superior colliculus interneuron spike width (ms) 4.2 ± 0.5 (8) 4.2 (ms) Data Table
Superior colliculus superficial layer neuron stratum griseum superficiale of superior colliculus interneuron spike half-width (ms) 1.8 ± 0.2 (8) 1.8 (ms) Data Table
Superior colliculus superficial layer neuron stratum griseum superficiale of superior colliculus interneuron AHP amplitude -21.0 ± 2.0 (8) 21.0 (mV) Data Table